目的:探讨低体重婴幼儿先天性心脏病手术治疗的适应症选择、体外循环管理及围术期处理。方法:全麻低温体外循环下对36例婴幼儿先天性心脏病患儿心脏缺损行缝合、修补、成形、疏通等手术治疗。结果:术后室间隔缺损补片修补残余分流2例,发生III0房室传导阻滞2例。除1例F4患儿死于术后低心排,其余均痊愈出院。结论:先天性心脏畸形应在婴幼儿时期予以矫治,精细的手术操作、良好的心肌保护和体外循环灌注是手术成功的关键。 Objective: To investigate the indications for surgical treatment of congenital heart disease in infants with low birth weight, cardiopulmonary bypass management and perioperative management. Methods: Under general anesthesia with hypothermic cardiopulmonary bypass, 36 cases of infants with congenital heart disease in children with cardiac defects suture, repair, shape, clear and other surgical treatment. Results: Ventricular septal defect patch repaired residual shunt in 2 cases, III0 atrioventricular block occurred in 2 cases. Except one case of F4 died of postoperative low cardiac output, the rest were cured. Conclusion: Congenital heart malformations should be corrected in infants and toddlers. Fine surgical procedures, good myocardial protection and cardiopulmonary bypass are the keys to successful operation.