家族性自发性气胸 (familialspontaneouspneumothorax ,FSP)是指家族中存在二人以上患有自发性气胸疾病。临床上较为少见 ,目前被认为是一种遗传疾病。作者自 1995年以来共治疗 4个FSP家族中 8位患者 ,总结如下。1　临床资料家族 1:男性 ,4 5岁 ,身高 172cm ,体重 6 3kg ,吸烟 Familial spontaneous pneumothorax (familialspontaneouspneumothorax, FSP) refers to the family of more than two people suffering from spontaneous pneumothorax disease. Clinically rare, is currently considered a genetic disease. The authors co-treated 8 of 4 FSP families since 1995, summarized below. 1 Clinical data Family 1: male, 4 5 years old, height 172cm, weight 6 3kg, smoking