烟雾病(Moyamoya disease,MMD)是先天性颅底血管发育异常或其他疾病导致的颅内血管异常血管网形成。该病的病理改变为颈内动脉终末段、大脑中动脉及大脑前动脉的起始部进行性狭窄或闭塞,早期尤以颈内动脉终末段狭窄多见,病变多数累及双侧。脑血管造影是确诊的金标准,但它是一项 Moyamoya disease (MMD) is an abnormal intracranial vascular network caused by congenital skull base dysplasia or other diseases. Pathological changes of the disease for the internal carotid artery segment, the middle part of the middle cerebral artery and anterior cerebral artery stenosis or occlusion, especially in the early stage of stenosis of the internal carotid artery more common, most lesions involving the bilateral. Cerebral angiography is the gold standard confirmed, but it is one