患儿女性， 6岁。因腹部膨隆 4a余收住院。患儿 2时家长发现其腹部较同龄儿童大，当时未予重视。 3岁时因腹部膨隆加重到当地医院就诊，发现“肝脾肿大”，诊断为“脾功能亢进”未予特殊处理。以后每 2mo复查一次“ B”超，提示肝脾进行性增大。近一年来腹部膨隆更加明显，行走 Children with children, 6 years old. Due to abdominal bulging more than 4a admitted to hospital. At 2 o’clock, the parents found that their abdomen was larger than their peers and was not valued at that time. 3 years old due to abdominal bulging aggravated to the local hospital for treatment and found that “hepatosplenomegaly”, diagnosed as “hypersplenism” was not given special treatment. After every 2mo review once “B” super, suggesting that the progressive increase of liver and spleen. Abdominal bulging in the past year more obvious, walking